Ureterocystoplasty (bladder augmentation) in a 16 year-old boy with Goldenhar syndrome

M.G. Scuderi, G. Milazzo, P. Betta, G. Spampinato, M. Fusco, M.C. Cutrupi, R. Chimenz, M. Falsaperla, V. Di Benedetto

Article ID: 6799
Vol 33, Issue 5S1, 2019
DOI: https://doi.org/10.54517/jbrha6799
Received: 8 November 2019; Accepted: 8 November 2019; Available online: 8 November 2019; Issue release: 8 November 2019

Abstract

The use of the dilated ureter for bladder augmentation is universally accepted for its lower rate of complications compared to the use of gastrointestinal segments. We report the case of a 16 yearold boy affected by Goldenhar syndrome who presented with neurogenic bladder with small-capacity, 5° grade vescico-ureteral reflux (VUR) with megaureter and bilateral hydronephrosis. Bladder augmentation using the distal dilated ureter, transuretero-ureterostomy left to right and Mitrofanoffs appendicovescicostomy were performed. Six months after surgery voiding cystourethrogram (VCUG) revealed a compliant bladder with a functional capacity of 400 ml. Ureterocystoplasty is a safe and effective method of augmenting small capacity urinary bladder. We suggest using the ureter, when available, instead of using gastrointestinal segments.


Keywords

bladder augmentation;ureterocystoplasty;neurogenic bladder


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