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Tetralogy of Fallot with an anomalous origin of right coronary artery from the pulmonary artery in a case of type A aortopulmonary window—A diagnostic challenge

Maruti Haranal, Shivang Saxena, Ashish Katewa

Article ID: 2343
Vol 4, Issue 1, 2023

DOI: https://doi.org/10.54517/ccr.v4i1.2343
VIEWS - 32 (Abstract)

Abstract

Aortopulmonary (AP) window is a conotruncal defect with an incidence of < 1% amongst congenital heart defects. It often occurs in association with other congenital cardiac defects. Coronary artery anomalies in association with the AP window are infrequent. An anomalous right coronary artery (RCA) from the pulmonary artery (ARCAPA) is an extremely rare entity with 0.002% incidence in the general population. To the best of our knowledge, the triad of Tetralogy of Fallot (TOF), ARCAPA and AP window is not yet reported in the literature.

Keywords

tetralogy; AP window; anomalous right coronary artery from the pulmonary artery

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References

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